Immune-deficient bronchiectasis associated with X-linked lymphoproliferative disease

Authors
Mehta, VK Massad, MG Tripathi, SP Koshy, M Geha, AS
Citation
Vk. Mehta et al., Immune-deficient bronchiectasis associated with X-linked lymphoproliferative disease, ANN THORAC, 68(2), 1999, pp. 578-580
Citations number
7
Categorie Soggetti
Cardiovascular & Respiratory Systems","Medical Research Diagnosis & Treatment
Journal title
ANNALS OF THORACIC SURGERY
ISSN journal
00034975 → ACNP
Volume
68
Issue
2
Year of publication
1999
Pages
578 - 580
Database
ISI
SICI code
0003-4975(199908)68:2<578:IBAWXL>2.0.ZU;2-D
Abstract
Bronchiectasis may occur with various congenital and acquired immunodeficie ncy diseases. The association of bronchiectasis and the X-linked lymphoprol iferative disease (XLP), also known as Duncan's disease is unknown. We desc ribe the case of a 39-year-old man with XLP, the oldest surviving, who deve loped chronic bronchiectasis with hemoptysis and required a pneumonectomy t o control his symptoms. (C) 1999 by The Society of Thoracic Surgeons.