Scimitar syndrome in infancy is a rare condition, presenting with severe co
ngestive heart failure and pulmonary hypertension. The presence of large sy
stemic-pulmonary collateral arteries may play a role in the cause of heart
failure and pulmonary hypertension. A 4-month-old infant underwent coil occ
lusion of large anomalous systemic arteries supplying the right lower pulmo
nary lobe. Symptoms of severe congestive heart failure and pulmonary hypert
ension improved dramatically with coil occlusion, and surgical correction w
as performed 3 months later without any complications. Coil occlusion of an
omalous systemic arteries can improve symptoms of heart failure and pulmona
ry hypertension in infants and may bring about a good surgical result for t
his disease.