Atrophy of the left lobe of the liver and anomalous hepatic vessel in a patient with Yunis-Varon syndrome

Yunis-Varon syndrome is inherited as an autosomal recessive trait. It is ch aracterized by facial and digit anomalies. This report describes a young wo man with clinical features of this syndrome, atrophy of the left lobe of th e liver, and a vascular anomaly. Liver abnormalities have not been describe d as features of this rare syndrome.