Monomelic amyotrophy: non progressive atrophy of the upper limb

Monomelic amyotrophy is a rare clinical entity, resulting in wasting and we akness localized to the hand and forearm unilaterally, in the absence of an y sensory or long tract signs. The onset of the disease is insidious, occur ring in males before the age of 30 years, with a clinical course marked by non-progression, The case of a 19-year-old Indonesian male patient is prese nted, with a one year history of right upper limb weakness. Nerve conductio n studies were normal, without evidence of conduction block. Electromyograp hy showed changes of chronic partial denervation. Magnetic resonance imagin g scans revealed an asymmetry of the spinal cord. Possible aetiological mec hanisms for these changes are discussed.