Superficial siderosis of the CNS due to chronic, recurrent subarachnoid hem
orrhage is an uncommon and potentially debilitating disorder. The classic c
linical manifestation is progressive bilateral sensorineural hearing loss (
SNHL), although ataxia and pyramidal signs also are observed frequently, Ca
vernous malformations rarely present with subarachnoid hemorrhage, We descr
ibe an unusual case of a young patient who presented with progressive, bila
teral SNHL who was found to have superficial CNS siderosis associated with
multiple cavernous malformations.