Aggressive form of pleural epithelioid haemangioendothelioma: complete response after chemotherapy

Epithelioid haemangioendotheliomas are rare tumours of endothelial origin. They can develop in any tissue but occur principally in the lung and liver. Their usual course is a slow progression, so that they can be treated by s urgery. In aggressive forms, no treatment has proved efficient to date, Thi s study, describes a case of bilateral pleural epithelioid haemangioendothe lioma that extended to the peritoneum. The histological diagnosis was confi rmed by both conventional examination and immunohistochemistry. After six c ourses of carboplatine plus etoposide, a complete response was obtained. Th e complete remission is still lasting at 18 months after the diagnosis and the patient is healthy.