Children with craniofacial anomalies are predisposed to airway obstruction
and frequently require airway intervention. Tracheotomy is performed when t
he airway obstruction is severe and refractory to other less invasive inter
ventions. Tracheotomy is associated with significant morbidity, and there i
s a trend noted in the literature toward achieving earlier decannulation by
the institution of definitive structural changes to the mandible. Mandibul
ar distraction osteogenesis has been shown to alleviate airway obstruction
in the pediatric population. We report a case in which mandibular distracti
on osteogenesis was successfully carried out in a neonate with acute airway
obstruction at birth as a result of combined Pierre Robin sequence and Kli
ppel-Feil syndrome. After 1 year, the patient still had an adequate airway
with tolerable scarring and no neurologic sequelae.