Congenital anomalies of the gastrointestinal tract are a significant cause
of morbidity in children and, less frequently, in adults. These abnormaliti
es include developmental obstructive defects of the small intestine, anomal
ies of the colon, anomalies of rotation and fixation, anorectal anomalies,
and intestinal duplications. Neonates with complete high intestinal obstruc
tion do not usually require further radiologic evaluation following radiogr
aphy, whereas those with complete low obstruction should, undergo a contras
t material enema examination. An upper gastrointestinal series must be perf
ormed in all patients with incomplete intestinal obstruction because manage
ment is different in each case. In low intestinal obstruction, ultrasonogra
phy (US) may help differentiate between small bowel obstruction and colonic
obstruction. In addition, US can help correctly identify meconium ileus an
d meconium peritonitis and is useful in the diagnosis of enteric duplicatio
n cysts. In malrotation and anorectal anomalies, computed tomography (CT) a
nd magnetic resonance (MR) imaging can provide superb anatomic detail and a
dded diagnostic specificity. Intestinal duplications manifest as an abdomin
al mass at radiography, contrast enema examination, or US. At CT, most dupl
ications manifest as smoothly rounded, fluid-filled cysts or tubular struct
ures with thin, slightly enhancing walls. At MR imaging, the intracystic fl
uid has heterogeneous signal intensity on Tl-weighted images and homogeneou
s high signal intensity on T2-weighted images. Familiarity with these gastr
ointestinal abnormalities is essential for correct diagnosis and appropriat
e management.