The association of hereditary palmoplantar keratoderma and idiopathic
clubbing of the digits in the same patient is uncommon. The differenti
al diagnosis includes the Bureau-Barriere-Thomas syndrome, primary pac
hydermoperiostosis, Fischer's and Volavsek's syndromes, and palmoplant
ar keratoderma Vorner. A 30-year-old woman with palmoplantar keratoder
ma and clubbing of the fingers since the age of 13 years is presented.