Choanal atresia is a relatively common congenital malformation which is oft
en associated with other anomalies. On the other hand, ileal atresia is ver
y rare, mostly nonsyndromic and occasionally associated with other anomalie
s. The association of choanal and ileal atresia is unknown. Here we report
the first instance of bilateral choanal atresia and ileal atresia in a full
term male infant and describe the subsequent surgical treatment of both co
nditions. The association is unique and may represent a syndrome. (C) 1999
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