Diagnosis, management, and pathophysiology of post-Fontan hypoxaemia secondary to Glenn shunt related pulmonary arteriovenous malformation

Authors
Premsekar, R Monro, JL Salmon, AP
Citation
R. Premsekar et al., Diagnosis, management, and pathophysiology of post-Fontan hypoxaemia secondary to Glenn shunt related pulmonary arteriovenous malformation, HEART, 82(4), 1999, pp. 528-530
Citations number
12
Categorie Soggetti
Cardiovascular & Respiratory Systems","Cardiovascular & Hematology Research
Journal title
HEART
ISSN journal
13556037 → ACNP
Volume
82
Issue
4
Year of publication
1999
Pages
528 - 530
Database
ISI
SICI code
1355-6037(199910)82:4<528:DMAPOP>2.0.ZU;2-V
Abstract
An 8 year old child with tricuspid atresia had developed right sided pulmon ary arteriovenous malformations following a previous classic Glenn procedur e. These became clinically manifest immediately after Fontan conversion bec ause of severe systemic desaturation. The pathophysiology and postoperative medical management of this case is described and related to current unders tanding of the aetiology of acquired pulmonary arteriovenous malformations following cavopulmonary shunt.