R. Premsekar et al., Diagnosis, management, and pathophysiology of post-Fontan hypoxaemia secondary to Glenn shunt related pulmonary arteriovenous malformation, HEART, 82(4), 1999, pp. 528-530
Citations number
12
Categorie Soggetti
Cardiovascular & Respiratory Systems","Cardiovascular & Hematology Research
An 8 year old child with tricuspid atresia had developed right sided pulmon
ary arteriovenous malformations following a previous classic Glenn procedur
e. These became clinically manifest immediately after Fontan conversion bec
ause of severe systemic desaturation. The pathophysiology and postoperative
medical management of this case is described and related to current unders
tanding of the aetiology of acquired pulmonary arteriovenous malformations
following cavopulmonary shunt.