Congenital orbital teratoma

A case of congenital orbital teratoma is described in which there was no or ganized eye only microscopic evidence of ocular tissues within the disorgan ized teratoma. A baby boy presented at birth with a 10-X-8-cm mass extrudin g from the left orbit. Magnetic resonance imaging (MRI) showed a mixed cyst ic-solid orbital mass containing areas of calcification and deforming the b ony orbit around its margins. There was no organized eye and no intracrania l extension. The eye was removed with reconstruction of the eyelids. Histop athology showed representation from all three germ cell layers consistent w ith a teratoma. There was no organized eye, but some disorganized ocular st ructures within the teratoma. Follow-up has been uneventful. Neonatologists and pediatricians should be aware of the possible diagnoses in a newborn p resenting with an orbital mass, so that early definitive surgery can be per formed with preservation of the globe where possible.