IgG anti-GQ1b antibody was present in a patient with acute ataxia and arefl
exia without ophthalmoplegia or elementary sensory loss. Sensory nerve cond
uction studies and somatosensory evoked potentials were normal, but postura
l body sway analysis showed dysfunction of the proprioceptive afferent syst
em. The clinical presentation and laboratory results for this patient resem
ble those of Miller Fisher syndrome, except for the lack of ophthalmoplegia
. This case may represent part of an IgG anti-GQ1b syndrome.