Sudden death in an adult with a small ventricular septal defect and an aneurysmal membranous septum

Citation
B. Sarubbi et al., Sudden death in an adult with a small ventricular septal defect and an aneurysmal membranous septum, CARD YOUNG, 9(1), 1999, pp. 99-103
Citations number
15
Categorie Soggetti
Pediatrics
Journal title
CARDIOLOGY IN THE YOUNG
ISSN journal
10479511 → ACNP
Volume
9
Issue
1
Year of publication
1999
Pages
99 - 103
Database
ISI
SICI code
1047-9511(199901)9:1<99:SDIAAW>2.0.ZU;2-F
Abstract
An apparently healthy man of 26 years of age suddenly died. He was known to have had a small ventricular septal defect and complete right bundle branc h block from early childhood. At post-mortem examination the small ventricu lar septal defect was found associated with an aneurysm of the membranous s eptum. Histological examination showed a normal atrioventricular node and b undle, adjacent to the aneurysm. There was fibrous interruption at the comm encement of the right bundle branch, which was considered the basis of the bundle branch block. It was also considered that the right bundle branch bl ock was of the hereditary type and that this, rather than the aneurysm of t he membranous septum, was responsible for the unexpected death.