Cervical extradural hematoma revealing hemophilia

Background. - Neurological hemorrhagic complications are unusual in hemophi liacs. Extradural hematoma is an exception, particularly at the cervical le vel. Less than 10 cases have been reported in the literature. We report a n ew case which was the inaugural sign of hemophilia A. Case report. - Moderate hemophila A was revealed by post-traumatic cervical extradural hematoma in a 12-year-old boy. Pain in the cervical spine and p rogressive tetraplegia led to the diagnosis, confirmed by cervical CT scan. The dissonance between the injury and the minor trauma led to hemostasis e xploration which revealed factor VIII at 3 %. After prompt correction of th e deficiency, total laminectomy allow removal of the hematoma. The neurolog ical course was satisfactory. Conclusion. - We stress the specific character of this association and the previously unreported mode of hemophilia disclosure. CT scan and MRI facili tate diagnosis allowing satisfactory course after emergency decompressive l aminectomy.