Hypoplastic left heart syndrome with right aortic arch, bilateral arterialducts and origin of the left subclavian artery from the left pulmonary artery

The rare association, in a left-sided heart with hypoplastic left heart syn drome, of right aortic arch, bilateral patent arterial ducts and origin of the left subclavian artery from the left pulmonary artery are described. Ca rdiac catheterization was performed because of the abnormal anatomy of the arch noted at echocardiographic examination. This abnormality is of surgica l importance when planning the Norwood operation.