Amyopathic dermatomyositis, also known as dermatomyositis sine myositis, de
scribes patients with the typical cutaneous features of dermatomyositis but
without evidence of inflammatory myopathy. There have been 3 reported case
s of amyopathic dermatomyositis associated with breast cancer in patients w
ith no prior malignancy. We describe the first case of paraneoplastic amyop
athic dermatomyositis associated with breast cancer recurrence.