The authors report the case of a 22-year-old man presenting with a tumour o
f the lower pole of the left testis present for 4 months, which proved to b
e a calcified Sertoli large cell tumour an extremely rare group of sex cord
tumours of the testis presenting specific clinical and histological featur
es. These tumours are usually benign, occur during the first two decades of
life and can be associated with dysplastic complexes or endocrinopathies (
Carney's complex, Peutz-Jeghers syndrome). They present either in the form
of bilateral, multifocal tumours in the context of a pathological associati
on, or in the unilateral form, without association. Several malignant forms
with metastases have been described. Conventional treatment is transinguin
al radical orchidectomy.