Large vestibular aqueduct syndrome (LVAS) is a common inner ear anomaly res
ponsible for some unusual vestibular and audiological symptoms. The gross a
ppearance of CT scan of the inner ear is generally normal. However, precise
measurement of the inner ear components reveals abnormal dimensions, which
may account for accompanying auditory or vestibular dysfunction. It has be
en reported that sudden increase in cerebrospinal fluid pressure can cause
further deterioration of healing due to transmission of pressure to the inn
er ear through the enlarged vestibular aqueduct. However, vestibular functi
on is not often studied. In this report, audiovestibular Function of 10 pat
ients with large vestibular aqueducts was analysed and compared with the se
verity of the radiological deformity. The literature was reviewed and typic
al findings were discussed to emphasize varying aspects of audiovestibular
function. It was found that some patients with LVAS have some spontaneous o
r provoked vestibular disturbance such as vertigo after watching revolving
objects. The mean value of electronystagmographic abnormality in patients w
ith hearing loss is greater than in patients with normal hearing. However,
there is no statistical correlation between the level of hearing loss. elec
tronystagmographic abnormality and severity of radiological deformity.