Primary orbital angiosarcoma: A case report

Purpose: The pathogenesis, natural history, histopathology, and recommended treatment for orbital angiosarcoma are illustrated and reviewed. Methods: Case report. Results: A 71-year-old white male presented with bluish discoloration and s welling of the left medial canthal area. A fine needle aspiration and excis ional biopsy with histopathologic examination was performed, which showed a ngiosarcoma. Pattern of growth was demonstrated radiographically and histop athologically, confirming primary orbital angiosarcoma. Subsequent wide sur gical resection was carried out, with substantial reconstruction of the lef t orbital and periorbital area. The patient responded well to the surgery, and was free of tumor after six years of follow-up. Conclusion: Angiosarcoma is a rare and highly malignant tumor of epithelial origin. The aggressive nature of this tumor usually results in a high mort ality rate despite treatment. However, early diagnosis and wide surgical ex cision has resulted in successful treatment of these tumors.