Idiopathic capillary hyperpermeability syndrome

BACKGROUND: Idiopathic capillary hyper permeability syndrome is expressed b y episodes of hypovolemic shock with normal consciousness. CASE REPORT: A 61-year-old man had a history of recurrent shock During the shock episodes, blood pressure was non-measurable and laboratory tests show ed polycytemia, low serum protein and monoclonal immunoglobulinemia, The pa tient also developed pnsumocytosis and had an infra-His block. DISCUSSION: The final diagnosis was idiopathic capillary hyperpermeability syndrome. This rare syndrome associates recurrent shock with Ige monoclonal immunoglobulinemia and, at the time of the shock episodes, increased hemat ocrit with paradoxical fall in serum protein.