T. Suzuki et al., IDIOPATHIC RESTRICTIVE CARDIOMYOPATHY WITH DIFFUSE PERIMYOCYTIC FIBROSIS - A RARE OBSERVATION, Japanese Circulation Journal, 61(3), 1997, pp. 272-274
Idiopathic restrictive cardiomyopathy (RCM) is rare. Even today little
is understood of its etiology or underlying mechanisms, and definitiv
e diagnostic criteria are lacking. In this report, we describe a case
of idiopathic RCM in a young Japanese woman who died while awaiting ca
rdiac transplantation during the 5-year course of the disease. Rare pa
thologic findings of diffuse perimyocytic fibrosis were revealed at au
topsy.