Angiosarcomas rarely involve the female genital tract. There have only been
sporadic case reports of angiosarcomas of the cervix, uterus, vagina, para
metrium, broad ligament and pelvis, and only 11 well-documented case report
s of primary ovarian angiosarcoma in the English language literature to dat
e. We present a case of primary pure ovarian angiosarcoma with lung metasta
sis that had partial response after chemotherapy with adriamycin and ifosfa
mide. But pulmonary hemorrhage and respiratory failure resulted in her deat
h 7 months after initial diagnosis.