We report on a 2.5-year old boy with severe mental retardation, choreoathet
osis, dystonia, muscle rigidity, opisthotonus and severe hearing impairment
. He had history of severe hyperbilirubinaemia immediately after birth pres
umably due to ABO incompatibility. The history and the clinical picture sug
gested the diagnosis of Kernicterus. The MR imaging examination upon admiss
ion revealed bilateral signal intensity increase in the globus pallidum on
T2-weighted sequences. Additionally, our patient showed signal intensity ch
anges within the subthalamic nuclei, which is known to be another character
istic area of bilirubin deposition in Kernicterus.