Only a few reports of primary cutaneous rhabdoid tumors have been published
. We describe the case of a S-month-old female patient who developed a rhab
doid type cutaneous sarcomatoid neoplasm in her upper back, close to a beni
gn myofibromatous proliferation of infancy. The lesion was studied both by
light microscopy and immunohistochemically. Flow cytometry was performed sh
owing a DNA diploid profile of the malignant tumor. The pathological findin
gs suggest a mesenchymal origin (hemangiopericytic or myofibroblastic type)
for both tumors. The patient was surgically treated, but she died nine mon
ths later.