Kaposiform hemangioendothelioma is a rare vascular neoplasm in children oft
en associated with Kasabach-Merritt syndrome. The tumor usually presents in
retroperitoneal location and is rarely present at birth. Cutaneous lesions
manifest after birth and must be clinically differentiated from infantile
hemangiomas and diffuse neonatal hemangiomatosis. Histologically, it bears
similarities with Kaposi sarcoma. We present a case of congenital cutaneous
multifocal kaposiform hemangioendothelioma (KHE).