This is a presentation of a case of tuberous sclerosis with multifocal hama
rtomas in the retroperitoneum, both kidneys, and the liver. Lymphangiectasi
a and numerous ectatic lymphatic channels penetrating through the retroperi
toneal angiomyolipoma were demonstrated by lymphography and computed tomogr
aphy. The findings in our study may document the presence of degenerative c
hange in the lymphatic system-not just in elastic vessels-an association wh
ich has not vet been reported in the radiological literature. (C) Elsevier
Science Inc., 1999.