NEONATAL SPORADIC HYPEREKPLEXIA - A RARE AND OFTEN UNRECOGNIZED ENTITY

We report the case of a newborn infant with transient generalized stif fness, obvious from the first days of life, increased muscle tone and repeated myoclonic jerks, who was unsuccessfully treated with phenobar bital until the diagnosis of neonatal sporadic hyperekplexia. To our k nowledge this is the first case successfully treated with clobazam, a 1.5 dibenzodiazepine. (C) 1997 Elsevier Science B.V.