INFANTILE POLYMYOSITIS WITH NORMAL SERUM CREATINE-KINASE LEVEL

Citation
S. Tutuncuoglu et al., INFANTILE POLYMYOSITIS WITH NORMAL SERUM CREATINE-KINASE LEVEL, Brain & development, 19(1), 1997, pp. 63-65
Citations number
10
Categorie Soggetti
Clinical Neurology
Journal title
ISSN journal
03877604
Volume
19
Issue
1
Year of publication
1997
Pages
63 - 65
Database
ISI
SICI code
0387-7604(1997)19:1<63:IPWNSC>2.0.ZU;2-6
Abstract
A 30-month-old boy who has been suffering progressive proximal muscle weakness and severe atrophy in shoulder and hip muscles from 11 months of age had prominent perivascular inflammatory cellular infiltration in his muscle biopsy and myopathic EMG changes. But his serum creatine kinase (CK) levels were repeatedly found to be within normal ranges. Oral prednisolone therapy (2 mg/kg/d) brought a complete recovery of m uscle power and normalization of EMG and muscle biopsy findings. This report provides an additional support that the cases of infantile poly myositis with normal serum CK levels may respond well to steroid thera py. (C) 1997 Elsevier Science B.V.