Thirty consecutive patients with congenital spinal deformity underwent magn
etic resonance imaging (MRI) to determine the incidence of occult intraspin
al anomaly. These congenital spinal deformities included 29 cases of congen
ital scoliosis and one case of congenital kyphosis. Physical examination fi
ndings and plain radiographs were reviewed in an attempt to correlate these
findings with subsequent intraspinal pathology. Nine patients had intraspi
nal anomalies identified on MRI consisting of five with tethered cord, four
with syringomyelia, three with lipoma, and one with diastematomyelia. One
patient required surgery for diastematomyelia; another underwent release of
his tethered cord. Only one patient, with diastematomyelia associated with
a syrinx and bifocal tethering, had his anomaly suggested by physical exam
ination and plain radiographs. Two other patients had findings on plain rad
iographs previously associated with high prevalence of occult intraspinal a
nomalies; one patient with congenital kyphosis had a tethered cord, and one
patient with a unilateral hemivertebrae associated with a contralateral ba
r had a tethered cord. Two of nine patients with occult intraspinal anomali
es required surgery for their anomaly. In patients with a congenital spinal
deformity, we found nine (30%) of 30 to have an associated anomaly within
the spinal canal. Only three of these nine had plain radiographs and physic
al examination findings suggestive of their subsequent MRI findings. Given
the poor correlation between findings on physical examination, plain radiog
raphs, and subsequent occult intraspinal anomalies on MRI, we believe that
MRI is helpful in evaluating patients with congenital spinal anomalies.