The case of a woman with short neuralgiform paroxysmal attacks located in o
rbital-periorbital area and associated with autonomic features of ten years
duration is reported. This headache syndrome is compared with trigeminal n
euralgia involving the first branch of the nerve. Duration, intensity, spre
ading of the pain and presence of accompanying ipsilateral vasomotor phenom
ena may be of help in the differential diagnosis. According to the latest r
eports, sex distribution which passed from 17 men/2 women to 18/6 and effec
t of the carbamazepine on pain would not appear to have an effect. Neverthe
less other reports are needed to distinguish these two clinical syndromes a
nd to develop an etiological and pathogenesis hypothesis.