Severe congenital hearing impairment is an important handicap affecting 0.1
% of apparently healthy liveborn int:ants and 1-2% of graduates of neonatal
intensive care units. The prognosis for intellectual, emotional, language
and speech development in the hearing-impaired child is improved when the d
iagnosis is made early and intervention is begun before the age of 6 mo. Un
iversal screening is preferable, since about 50% of infants with hearing lo
ss are not discovered if neonatal hearing screening is restricted to high-r
isk groups. The automated auditory brainstem response (AABR) screener is a
dedicated hearing screening device which provides information not only abou
t the outer/middle ear and cochlea but also about the auditory pathway up t
o the brainstem. AABR has an agreement with conventional auditory brainstem
response up to 98%. It uses a 35 dB near hearing level click. No operator
interpretation is needed and it can be used on the ward and during oxygen t
herapy without disturbance from ambient noise. Reported referral rates in a
hospital-based screening programme at the time of discharge vary, with an
average of 4%. AABR has also been used in a home-based setting, with the sa
me results. The time necessary for screening varies with the setting, but r
anges from 4 to 15 min. Initial costs range from $15 to $25 per test, which
is similar to neonatal screening for metabolic diseases. In addition to in
dividual healthcare savings. early diagnosis may lead to savings on costs o
f intensive speech-language intervention and educational facilities.