Linear scleroderma 'en coup de sabre' is characterized by atrophy and furro
wing of the skin of the frontoparietal region. In most cases it occurs as a
single, paramedian line that may be associated with hypoplasia of underlyi
ng structures and hemiatrophy of the face. Rarely, lesions form two lines,
either both on the same side or bilaterally. We describe an 18-year-old mal
e with an unusual tri-linear pattern of scleroderma 'en coup de sabre' foll
owing Blaschko's lines.