We reported a 5-years old boy with frosted branch angiitis in both eyes. Th
e Visual acuities of the two eyes were suddenly lost to 5/50. The fluoresce
in angiography, electroretinograms (ERGs) and pattern evoked potentials (PV
EPs) had been tested at the acute and the recovery stage of the disease. At
the onset of the disease, fluorescein angiography showed obvious dye leaka
ge from dilated retinal veins. The PVEPs and whole field ERGs including rod
, maximum, OPs and cone responses were seriously decreased and prolonged, i
ndicating that the visual pathway's and retinal functions were greatly dama
ged. The patient had an excellent response to systemic prednisone. One mont
h after the treatment, the Visual acuities recovered to 60/50 in both eyes.
The fluorescein angiography showed that leakage from blood vessels was dim
inished, but the lesions at macula and optic disc were persisted a longer t
ime even to the end of treatment. Through 6 months medication, nearly all o
f the electrophysiological abnormalities had been resolved.