Basaloid follicular hamartoma is not a well-recognized clinical entity and
has often been diagnosed as trichoepithelioma or basal cell carcinoma. It i
s a unique benign follicular tumour which comprises a variety of clinical m
anifestations. We present the case of a 24-year-old male with unilateral ba
saloid follicular hamartoma present at birth and later misdiagnosed as basa
l cell carcinoma. Histological features of basaloid follicular hamartoma ar
e nor always diagnostic and clinico-pathological correlation is particularl
y important to distinguish this benign hamartoma from other basaloid tumour
s including basal cell carcinoma. Continuous follow-up of our patient did n
ot reveal any clinical or histological malignant transformation. (C) 1999 E
lsevier Science B.V. All rights reserved.