Takayasu's disease is an arteritis with a predilection for the proximal bra
nches of the aortic arch. Chronic retinal hypoxic changes and ischemic ocul
ar inflammation, resulting from cervical vascular occlusion, have been exte
nsively described. Anterior ischemic optic neuropathy has rarely been repor
ted in this condition, and only in conjunction with other ophthalmic findin
gs. The authors present the case of a 25-year-old woman who developed unila
teral anterior ischemic optic neuropathy in the absence of other eye findin
gs and was subsequently found to have an aortic arch syndrome compatible wi
th Takyasu's disease.