Pulmonary manifestations of Crohn's disease are infrequent in adults and ev
en less common in children. Our literature search found only a few cases of
Crohn's disease causing pulmonary manifestations in children. We report on
the case of a 13-year-old girl in whom severe pulmonary disease was found
four years after the onset of Crohn's disease. Open lung biopsy uncovered b
ronchiolitis obliterans and granulomatous lung disease. Aggressive treatmen
t has yielded gradual improvement. This case emphasizes the importance of r
ecognizing the association, the differential diagnosis, and treatment impli
cations. Pediatr Pulmonol. 2000; 29:151-154, (C) 2000 Wiley-Liss, Inc.