Dysembryoplastic neuroepithelial tumor (DNT) is an uncommon intracranial tu
mor which is usually encountered in patients with medically intractable com
plex partial seizures of temporal lobe origin. Melanotic differentiation in
a DNT has not been reported previously Herewith we report a case of DNT wi
th unique melanotic differentiation in a 23-year-old female who presented w
ith medically intractable epilepsy. She underwent craniotomy and tumor deco
mpression with a good outcome. We present the histopathological features of
DNT with melanotic differentiation and discuss its prognostic significance
.