The case history is described of an adolescent girl with alveolar rhabdomyo
sarcoma of the maxillary sinus, who was treated with radical radiotherapy a
nd adjuvant chemotherapy. She relapsed in the breast and, after incomplete
excision, received radical radiotherapy resulting in long-term survival wit
h breast conservation. The characteristics of patients with metastatic rhab
domyosarcoma with breast involvement are discussed. In adolescent girls, th
e breast is postulated to be a preferential metastatic site.