Non-convulsive status in the ring chromosome 20 syndrome: a video illustration of 3 cases

We report the clinical history and the video-EEG recordings of three young adults with r(20), who exibited repeated episodes of nonconvulsive status e pilepticus, often triggered by emotional events. This recognizable clinical entity associates a slight mental deficiency, be havioural disorder and epilepsy, often resistant to treatment and with a pa rticular clinical presentation. We demonstrate with video EEC recording, atypical absence status triggered by emotional behaviour with ictal EEC characterized by bifrontal slow waves , often rhythmic, or sharp waves. Our report highlights the characteristic features of non-convulsive status in this electro-clinical syndrome.