Biventricular implantable cardioverter defibrillator use in a patient withheart failure and ventricular tachycardia secondary to Emery-Dreifuss syndrome

We report a case of fully transvenous single-unit biventricular implantable cardioverter defibrillator (ICD) use in a 43-year-old woman with a manifes ting carrier form of muscular dystrophy (Emery-Dreifuss syndrome). The indi cation for biventricular ICD use was progressive heart failure with ventric ular arrhythmia, permanent atrial fibrillation and previous VVIR pacemaker insertion. Single-unit transvenous biventricular ICD implantation was under taken without complication. No potentially serious device malfunction was n oted during subsequent follow-up. We conclude that single-unit biventricula r ICD implantation is feasible for pacing and ventricular tachyarrhythmia c ontrol in patients with underlying atrial fibrillation.