ANEURYSMAL ARTERIAL-DISEASE IN A PATIENT WITH EHLERS-DANLOS-SYNDROME - CASE-REPORT AND LITERATURE-REVIEW

Multiple aneurysmal lesions and dissections of the right femoral arter y in a young man with type IV Ehlers-Danlos syndrome are presented. Ty pe IV results in a high incidence of vascular lesions - extreme fragil ity of arteries is associated with multiple aneurysm formation and spo ntaneous rupture and dissection of arteries. Surgical management of pa tients with this disorder is hazardous and often unrewarding. The succ essful surgical treatment of an. acutely thrombosed aneurysmal femoral artery by means of an interposition graft, is presented and brief gui delines for the treatment and prevention of vascular complications are discussed.