Hernia uterus inguinale in a 46,XX female - A case report

BACKGROUND: Hernia uterus inguinale, a rare congenital anomaly, is usually found in hermaphrodites. CASE: A case of lateral fusion defect associated with mullerian duct develo pment in a young women with primary amenorrhea and normal karyotype occurre d. In our patient, bilateral mullerian? duct systems were rudimentary and f ailed to fuse in the midline. The left horn Of the uterus and ipsilateral o vary lay in the left inguinal canal. The right horn of the uterus, along wi th the tribe and ovary, was intraabdominal. CONCLUSION: In the operative management of this rare anomaly, care must be taken to preserve and reposition the ovary in the abdominal cavity.