A case report of caudal regression syndrome associated with an intraspinalarachnoid cyst

We report here a rare case of caudal regression syndrome associated with an intraspinal arachnoid cyst, The patient was a 6-month-old baby girl with m ulticomplex congenital abnormalities: sacrococcygeal dysgenesis and ventral curvature, large terminal cyst (myelocystocele), spinal arachnoid cyst, ce rebellar hypertrophy (suspected), high imperforate anus, partial dysgenesis of the large intestine, omphalocele, atresia of the vagina, bilateral inco mplete ureter duplication, incomplete pseudo-duplicated bladder and bilater al talipes equinovarus. We performed plastic repair of the myelocystocele a nd perineal lesion for caudal regression syndrome and partial removal of th e cyst wall for the intraspinal arachnoid cyst. She has been well for 3 yea rs postoperatively, and her mental development is normal. Copyright (C) 200 0 S. Karger AG, Basel.