A 36-year old woman was presented to our hospital with congenital ventricul
ar septal defect and one-vessel coronary artery disease (75% proximal left
main coronary artery) for CABG and repair of the VSD. After induction,a tra
nsesophageal echocardiographic (TEE) baseline examination was performed, sh
owing a severely dilated coronary sinus (CS) measuring approximately 3 cm (
abnormal >1 cm). We suggested a persist ent left superior vena cava (PLSVC)
draining into the CS. PLSVC is a common venous congenital anomaly, with a
reported incidence of 0.5% in general population and in 3-5 % of patients w
ith congenital heart defect. Injection of echo-contrast solution in a left
arm vein,visualizing microbubbles passing through the PLSVC into the CS con
firmed our suspicion. The diagnosis of a PLSVC and dilated CS is a contrain
dication for retrograde cardioplegia because of the loss of cardioplegia in
to the PLSVC resulting in a inadequate myocardial protection. It may be dif
ficult to pass a pulmonary artery catheter (PAC) through a left internal or
left subclavian vein and it may be associated with arrythmias. A chest rad
iograph shows the anomalous course of the PAC along the left heart.