Wilms' tumor of the cervix: A case report and review of the literature

Introduction. Extrarenal Wilms' tumors are rare, with only 55 well-document ed cases in the literature and only 4 confined to the uterus. A fifth case along with review of the current literature is presented. Case. A 13-year-old girl presented with a 2-month history of irregular vagi nal spotting. A 6.5 x 4.5 x 2.5-cm polypoid mass meeting criteria for an ex trarenal Wilms tumor was removed from the superior aspect of the cervix, bu t recurred 8 months later on the posterior lip. The patient underwent a Sch auta procedure, lymph node dissection, and bilateral oophoropexy. The surge ry was followed by typical renal Wilms' tumor chemotherapy. The patient is without evidence of disease 5 years after surgery. Discussion. This case uniquely suggests that limited excision of the origin al tumor has inherent risks for relapse. Oophoropexy appears to be reasonab le when fertility preservation is desired and reconfirms that treatment mim icking renal nephroblastomas offers good long-term survival. (C) 2000 Acade mic Press.