Progressive spontaneous herniation of the thoracic spinal cord: Case report

OBJECTIVE AND IMPORTANCE: We report one case of spontaneous thoracic spinal cord herniation. To our knowledge, this is the first case involving radiol ogical documentation of the development of herniation. Clinical features an d surgical techniques are also presented. CLINICAL PRESENTATION: We describe the case of a 51-year-old female patient who experienced progressive Brown-Sequard syndrome for 2 years. Three magn etic resonance imaging examinations were performed; they revealed the progr essive development of anterolateral spinal cord herniation at the level of T6 during those 2 years. INTERVENTION: After laminectomy at T6, the herniated myelon was microsurgic ally removed and the neurological symptoms improved. CONCLUSION: We present the possible causes, the proposed pathophysiological mechanisms, and the clinical and radiological development of this rare ent ity, with a review of the literature published to date. We propose that a p reexisting weakness of the ventral dural fibers, combined with abnormal adh esion of the spinal cord to the anterior dural sleeve, leads to progressive herniation throughout life. Microsurgical treatment may halt the exacerbat ion of the neurological symptoms.