We report the case of a child with hypoplastic left heart syndrome who deve
loped pulmonary arteriovenous (AV) malformations after superior cavopulmona
ry anastomoses. Resolution of the pulmonary AV malformations occurred follo
wing a completion Fontan procedure. This phenomenon has been reported previ
ously, but only in patients with heterotaxy and polysplenia. (C) 2000 by Th
e Society of Thoracic Surgeons.