Congenital anomalies of the aortic valve can be associated with other cardi
ac anomalies. In this report, we present a patient with an aortic valve ano
maly associated with occlusion of left coronary ostia. In addition, we revi
ewed the literature and found 10 similar cases. Although compatible with li
fe, this anomaly can lead to significant symptoms. Preoperative diagnosis a
s well as proper therapeutic planning should be tailored to correct valvula
r competence and restore coronary blood flow. (C) 2000 by The Society of Th
oracic Surgeons.