Congenital cystic adenomatoid malformation (CCAM) of the lung is an uncommo
n congenital anomaly, especially in young adults. This study reports an 18-
yr-old male with CCAM I involving the right upper lobe, who presented with
a moderate spontaneous haemopneumothorax initially. The patient also had bi
lateral abdominal cryptorchidism which required surgical treatment earlier
in childhood. The chest radiographs and contrast-enhanced computed tomograp
hic scan of the chest shelved a multicystic lesion with air-fluid levels in
the right upper lung. The right upper lobe was resected through a posterol
ateral thoracotomy. Histological examination confirmed the diagnosis of CCA
M.
To the authors' knowledge, congenital cystic adenomatoid malformation prese
nting with spontaneous haemopneumothorax and haemoptysis has never been des
cribed in the literature.